A complex pancreaticobiliary malunion causing recurrent pancreatitis in a boy: A case report

Authors

  • Amen Zafar Shifa College of Medicine
  • Anwar Ul Haq Shifa International Hospital
  • Dawood Shehzad Rawalpindi Medical University
  • Mohammad Salih Shifa International Hospital
  • Gulrez Umar Rawalpindi Medical University

DOI:

https://doi.org/10.46831/jpas.v2i1.119

Keywords:

Congenital pancreaticobiliary maljunction, Pancreatolithiasis, Pancreaticobiliary reflux

Abstract

Background

Pancreaticobiliary malunion (PBM) is a distinct malformation of the pancreatic and biliary ductal system, in which the junction of the pancreatic and biliary ducts occurs above the duodenal wall. PBM has varied presentations that prompt early diagnosis and management.

Case Presentation

A 9-year-old male, a known case of chronic pancreatitis, presented with sudden intense abdominal pain and vomiting. After evaluation, the diagnosis of acute on chronic pancreatitis secondary to PBM was made and the patient underwent Roux-en y hepaticojejunostomy, along with cholecystectomy and common bile duct excision. 

Conclusion 

The purpose of this report is to add to the literature the unique presentation of PBM in the pediatric population in order to aid in prompt diagnosis and management. This will be the first report on PBM in the pediatric population of Pakistan

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Author Biographies

Amen Zafar, Shifa College of Medicine

5th Year Medical Student

Anwar Ul Haq, Shifa International Hospital

Consultant Pediatric Surgeon

Dawood Shehzad, Rawalpindi Medical University

5th Year Medical Student

Mohammad Salih, Shifa International Hospital

Cosultant Gastroenterologist and Hepatologist

Gulrez Umar, Rawalpindi Medical University

5th Year Medical Student

References

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Kamisawa T, Ando H, Suyama M, Shimada M, Morine Y, Shimada H, et al. Japanese clinical practice guidelines for pancreaticobiliary maljunction. J Gastroenterol [Internet]. 2012 [cited 2022 Jan 8]; 47(7):731–59.

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Published

2022-04-19

How to Cite

1.
Amen Zafar, Anwar Ul Haq, Dawood Shehzad, Mohammad Salih, Gulrez Umar. A complex pancreaticobiliary malunion causing recurrent pancreatitis in a boy: A case report . J Pediatr Adolesc Surg [Internet]. 2022Apr.19 [cited 2022Aug.7];2(1). Available from: http://jpedas.org/ojs/index.php/jpedas/article/view/119
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