A complex pancreaticobiliary malunion causing recurrent pancreatitis in a boy: A case report
DOI:
https://doi.org/10.46831/jpas.v2i1.119Keywords:
Congenital pancreaticobiliary maljunction, Pancreatolithiasis, Pancreaticobiliary refluxAbstract
Background
Pancreaticobiliary malunion (PBM) is a distinct malformation of the pancreatic and biliary ductal system, in which the junction of the pancreatic and biliary ducts occurs above the duodenal wall. PBM has varied presentations that prompt early diagnosis and management.
Case Presentation
A 9-year-old male, a known case of chronic pancreatitis, presented with sudden intense abdominal pain and vomiting. After evaluation, the diagnosis of acute on chronic pancreatitis secondary to PBM was made and the patient underwent Roux-en y hepaticojejunostomy, along with cholecystectomy and common bile duct excision.
Conclusion
The purpose of this report is to add to the literature the unique presentation of PBM in the pediatric population in order to aid in prompt diagnosis and management. This will be the first report on PBM in the pediatric population of Pakistan
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References
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Copyright (c) 2022 Amen Zafar, Anwar Ul Haq, Dawood Shehzad, Mohammad Salih, Gulrez Umar
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