Functional retrocaval paraganglioma: A case report

Authors

  • dilip kumar pal Professor and Head, Department of Urology
  • Debansu Sarkar
  • Mrinal Tandon

DOI:

https://doi.org/10.46831/jpas.v2i2.147

Keywords:

Functional, Paraganglioma, Retrocaval, Surgical resection

Abstract

Background: Functional paragangliomas are one of the rare and curable causes of secondary hypertension. Its usual location is in the region of the head and neck but is rarely seen in the retrocaval region.

Case Presentation: We present a rare case of an 18-year-old young boy who presented with functional retrocaval paraganglioma. The Imaging workup revealed a 6cm mass abutting the inferior vena cava (IVC). The mass was successfully excised. Histopathology showed it was a paraganglioma.

Conclusion: Retroperitoneal retrocaval paragangliomas are rarely seen tumors with very few cases reported so far. The location of paragangliomas in this region is usually uncommon and its surgical resection is itself a challenge for the surgeon. Complete surgical resection with prior adequate hypertension control is the only curative treatment of paragangliomas. Lifelong follow-up is necessary to detect early recurrence

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Author Biography

dilip kumar pal, Professor and Head, Department of Urology

Institute of Post Graduate Medical Education and Research (IPGME&R), Kolkata

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Published

2023-09-11

How to Cite

1.
pal dilip kumar, Sarkar D, Tandon M. Functional retrocaval paraganglioma: A case report. J Pediatr Adolesc Surg [Internet]. 2023Sep.11 [cited 2024Apr.17];2(2). Available from: http://jpedas.org/ojs/index.php/jpedas/article/view/147
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