Congenital biliary web- a rare cause of obstructive jaundice in an infant: A case report
Keywords:Congenital biliary web, Obstructive jaundice, Biliary atresia, Stricture
Background: Congenital biliary web of the extra-hepatic biliary tree is becoming exceedingly rare cause of obstructive jaundice in children.
Case Presentation: We report a case of 5-month-old male baby who presented with acholic stools and persistent jaundice since birth. Magnetic resonance cholangiopancreatography (MRCP) showed contracted gall bladder and focal narrowing at mid portion of the common bile duct (CBD) with proximal dilatation of biliary channels. On exploration, a complete web was found just proximal to the confluence of cystic duct and common hepatic duct causing complete obstruction of biliary tree. A Roux-en-Y hepatico-jejunostomy was done. Postoperative recovery was uneventful.
Conclusion: We conclude that congenital biliary web is a rare entity and should be considered in the differential diagnosis of biliary atresia.
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Copyright (c) 2020 Allah Ditta, Dr. Muhammad Bilal Mirza, Muhammad Waqas-ur-Rehman, Maria Fahim, Farrakh Mehmood Satar, Nabila Talat
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