Congenital biliary web- a rare cause of obstructive jaundice in an infant: A case report

Authors

  • Allah Ditta Department of Pediatric Surgery, The Children’s Hospital & the Institute of Child Health, Lahore
  • Dr. Muhammad Bilal Mirza Department of Pediatric Surgery, The Children's Hospital and the Institute of Child Health, Lahore https://orcid.org/0000-0003-1389-8756
  • Muhammad Waqas-ur-Rehman The Children’s Hospital & the Institute of Child Health, Lahore.
  • Maria Fahim Department of Pediatric Surgery, The Children's Hospital and the Institute of Child Health, Lahore
  • Farrakh Mehmood Satar Department of Pediatric Surgery, The Children's Hospital and the Institute of Child Health, Lahore
  • Nabila Talat Department of Pediatric Surgery, The Children's Hospital and the Institute of Child Health, Lahore

DOI:

https://doi.org/10.46831/jpas.v1i1.7

Keywords:

Congenital biliary web, Obstructive jaundice, Biliary atresia, Stricture

Abstract

Background: Congenital biliary web of the extra-hepatic biliary tree is becoming exceedingly rare cause of obstructive jaundice in children.

Case Presentation: We report a case of 5-month-old male baby who presented with acholic stools and persistent jaundice since birth. Magnetic resonance cholangiopancreatography (MRCP) showed contracted gall bladder and focal narrowing at mid portion of the common bile duct (CBD) with proximal dilatation of biliary channels. On exploration, a complete web was found just proximal to the confluence of cystic duct and common hepatic duct causing complete obstruction of biliary tree. A Roux-en-Y hepatico-jejunostomy was done. Postoperative recovery was uneventful.

Conclusion: We conclude that congenital biliary web is a rare entity and should be considered in the dif­ferential diagnosis of biliary atresia.

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Author Biographies

Allah Ditta, Department of Pediatric Surgery, The Children’s Hospital & the Institute of Child Health, Lahore

Postgraduate Resident of MS

Dr. Muhammad Bilal Mirza, Department of Pediatric Surgery, The Children's Hospital and the Institute of Child Health, Lahore

Asst. Professor of Pediatric Surgery Unit-II

Maria Fahim, Department of Pediatric Surgery, The Children's Hospital and the Institute of Child Health, Lahore

Post-graduate Resident of Pediatric Surgery

Farrakh Mehmood Satar, Department of Pediatric Surgery, The Children's Hospital and the Institute of Child Health, Lahore

Consultant

Nabila Talat, Department of Pediatric Surgery, The Children's Hospital and the Institute of Child Health, Lahore

Professor of Paediatric Surgery Unit-II

References

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Published

2020-08-21

How to Cite

1.
Ditta A, Mirza MB, Waqas-ur-Rehman M, Fahim M, Satar FM, Talat N. Congenital biliary web- a rare cause of obstructive jaundice in an infant: A case report. J Pediatr Adolesc Surg [Internet]. 2020Aug.21 [cited 2020Oct.28];1(1):47-9. Available from: http://jpedas.org/ojs/index.php/jpedas/article/view/7
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