Solitary intrascrotal neurofibroma in a child: A case report

Authors

  • Ghadir Jaber Consultant Pediatric surgeon
  • Vipul Gupta Senior Specialist Registrar
  • Usman Javaid Senior Specialist
  • Diary Mohammed Consultant Paediatric Surgeon
  • Mamoun AlMarzouqi Consultant Paediatric Surgeon

DOI:

https://doi.org/10.46831/jpas.v1i2.45

Abstract

Background: Neurofibroma (NF) remains a rare entity among various scrotal masses in the pediatric age group. We report a case of solitary intrascrotal extra testicular plexiform neurofibroma in a 6-year-old child with the clinical management of this rare entity and review of the literature.  

Case Summary: A 6-year-old male presented with incidentally noticed intrascrotal swelling. Clinical examination confirmed the presence of solitary intrascrotal swelling with normal testis. Radiological imaging showed the presence of a hypoechoic mass in the left hemiscrotum with normal both testes. Surgical exploration showed the presence of unencapsulated soft tissue mass and histopathological examination (HPE) confirmed the diagnosis of plexiform neurofibroma. Thorough evaluation ruled out features of neurofibromatosis 1 thus confirming the diagnosis of solitary intrascrotal extratesticular plexiform neurofibroma. Complete surgical excision resulted in satisfactory recovery with no recurrence on follow-up

Conclusion: Neurofibroma although rare should be considered as a differential in the diagnosis of an intrascrotal mass in the pediatric age group. The benign nature of the lesion and extratesticular origin usually makes testis sparing surgical excision feasible which remains the treatment of choice with excellent prognosis and minimal chances of recurrence. A thorough histopathological examination is mandatory to rule out neurofibromatosis.

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Published

2021-03-25

How to Cite

1.
Jaber G, Gupta V, Javaid U, Mohammed D, AlMarzouqi M. Solitary intrascrotal neurofibroma in a child: A case report. J Pediatr Adolesc Surg [Internet]. 2021Mar.25 [cited 2021May9];1(2). Available from: https://jpedas.org/ojs/index.php/jpedas/article/view/jpas-45
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