Every tangle has a story - Rapunzel Syndrome: A case report

Authors

  • Yousuf Aziz Khan
  • Zainab Zaib Ayub Teaching Hospital – MTI, Abbottabad
  • Fizza Tufail Ayub Teaching Hospital - MTI, Abbottabad
  • Kashif Rafiq Ayub Teaching Hospital - MTI, Abbottabad
  • Khyal Muhammad Ayub Teaching Hospital - MTI, Abbottabad

DOI:

https://doi.org/10.46831/jpas.v2i1.113

Keywords:

Rapunzel Syndrome, Trichobezoar, Epigastric mass, Paediatric

Abstract

Background: Rapunzel syndrome is the rarest form of trichobezoar; a condition in which trichobezoar extends beyond the stomach into the small intestine. It is common among children and young girls with a history of psychiatric illnesses.

Case Presentation: A 10-year-old girl without any history of psychiatric illness, presented with abdominal pain and non-bilious vomiting for 6 months. Clinically she had a non-tender upper abdominal mass which, later at workup, was found to be a trichobezoar.  She was surgically managed successfully.

Conclusion: Though uncommon, Rapunzel syndrome should be kept in the differential diagnoses especially in a young female patient with features of an upper GI obstruction and a non-tender, palpable epigastric mass.

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Author Biographies

Zainab Zaib, Ayub Teaching Hospital – MTI, Abbottabad

Post-graduate Resident - General Surgery

Department of Surgery, Surgical Unit A

Fizza Tufail, Ayub Teaching Hospital - MTI, Abbottabad

Intern - Paediatric Surgery

Department of Surgery, Surgical Unit A

Kashif Rafiq, Ayub Teaching Hospital - MTI, Abbottabad

Assistant Professor – General Surgery,

Department of Surgery, Surgical Unit A

Khyal Muhammad, Ayub Teaching Hospital - MTI, Abbottabad

Consultant Paediatrician

Department of Paediatrics, Paediatric Unit A

References

De Melio J, Debrouwere T, Herman M. Trichobezoar. J Belg Soc Radiol. 2021; 105:31.

Mouffak A, Salam S, Fahl A, Chbani K, Laoudiyi D, Ouzidane L. Rare cause of mechanical occlusion in children: a case report. Pan Afr Med J. 2021; 38:71.

Reilly L. Interesting cases in Pediatric Radiology: ingestions, insertions, and aspirations. J Radiol Nurs. 2021; 40:14-22.

Mazzei A, Centonze A, Aloi IP, Bertocchini A, Baldassarre E. Rapunzel Syndrome: endoscopy, laparotomy, or laparoscopy? J Indian Assoc Pediatr Surg. 2021; 26:66-7.

Kumar M, Maletha M, Bhuddi S, Kumari R. Rapunzel Syndrome in a 3-year-old boy: A menace too early to present. J Indian Assoc Pediatr Surg. 2020; 25:112-4.

Mirza MB, Talat N, Saleem M. Gastrointestinal trichobezoar: An experience with 17 cases. J Pediatr Surg. 2020; 55:2504-9.

Michael G, Qureshi E, Miah M, Husain N. An unusual form of a trichobezoar causing a peculiar case of appendicitis: A case of Rapunzel syndrome. Cureus. 2020; 12:e7554. Available from: https://doi.org/10.7759/cureus.7554.

Prasad A, Jain A, Gupta A, Kamra A. Trichobezoar: ravenous for hair. Euroasian J Hepatol Gastroenterol. 2018; 8:97-8.

Radhakrishna V, Basavaraju M. Laparoscopic extraction of a Rapunzel: Safe and effective. Gut. 2020; 69:A1–A95.

Antunes H, Barroso C, Faria C, Correia-Pinto J. Images in pediatrics: Rapunzel syndrome: the pathway for a prompt diagnosis. Arch Dis Child. 2020; 105:298.

Claro M, Costa Santos D, Abreu Silva A, Deus C, Grilo J, Sousa D, et al. When eating makes you sick - Gastric stump obstruction caused by a phytobezoar. A case report and literature review. Int J Surg Case Rep. 2021; 79:263-6.

Kang SK, Kim SH, Cho YH. Successful laparoscopic removal of a huge trichobezoar in cases of Rapunzel Syndrome in children. J Acute Care Surg. 2021; 11:39-42.

Published

2022-02-09

How to Cite

1.
Aziz Khan Y, Zaib Z, Tufail F, Rafiq MK, Muhammad K. Every tangle has a story - Rapunzel Syndrome: A case report. J Pediatr Adolesc Surg [Internet]. 2022Feb.9 [cited 2022Aug.7];2(1). Available from: http://jpedas.org/ojs/index.php/jpedas/article/view/jpas-113
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