Every tangle has a story - Rapunzel Syndrome: A case report
DOI:
https://doi.org/10.46831/jpas.v2i1.113Keywords:
Rapunzel Syndrome, Trichobezoar, Epigastric mass, PaediatricAbstract
Background: Rapunzel syndrome is the rarest form of trichobezoar; a condition in which trichobezoar extends beyond the stomach into the small intestine. It is common among children and young girls with a history of psychiatric illnesses.
Case Presentation: A 10-year-old girl without any history of psychiatric illness, presented with abdominal pain and non-bilious vomiting for 6 months. Clinically she had a non-tender upper abdominal mass which, later at workup, was found to be a trichobezoar. She was surgically managed successfully.
Conclusion: Though uncommon, Rapunzel syndrome should be kept in the differential diagnoses especially in a young female patient with features of an upper GI obstruction and a non-tender, palpable epigastric mass.
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Copyright (c) 2022 Yousuf Aziz Khan, Zainab Zaib, Fizza Tufail, Kashif Rafiq, Khyal Muhammad
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