Rectal atresia with pouch colon without fistula in a female newborn– a rare association: A case report

Authors

  • Dinesh Kumar Barolia Senior resident
  • Aditya Pratap Singh Department of Paediatric Surgery, Bhagwan Mahavir Hospital, Mahavir Nagar
  • Harsha Vinod Bathia Department of Anaesthia, Bhagwan Mahavir Hospital, Mahavir Nagar, Sumerpur
  • Vipal H Parmar Consultant histopathologist at neuberg supratech references laboratories, Ahmedabad (NSRL)
  • Bhavana Asit Mehta Department Histoanatomic Pathology Department, Neuberg Supratech Reference Laboratory, Ahmedabad, Gujarat
  • Shraddha Mehta Department Of Pathology, Bhagwan Mahavir Hospital, Mahavir Nagar, Sumerpur

DOI:

https://doi.org/10.46831/jpas.v2i1.102

Keywords:

Atresia, Anorectal malformation, Congenital pouch colon, Rectal atresia

Abstract

Background: Rectal atresia is a rare variant of anorectal malformation (ARM). Pouch colon is an abnormal dilation of the colon distally connected by the fistula. Pouch colon without fistula is extremely rare.

Case Presentation: We report a case of unusual association of rectal atresia with pouch colon without fistula in a female newborn. At surgery, a type IV pouch colon was found which was resected and colostomy was done as the initial procedure.

Conclusion: Rectal atresia with congenital pouch colon without genitourinary fistula in a female child is an extremely rare association.

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Author Biographies

Aditya Pratap Singh, Department of Paediatric Surgery, Bhagwan Mahavir Hospital, Mahavir Nagar

Consultant

Harsha Vinod Bathia, Department of Anaesthia, Bhagwan Mahavir Hospital, Mahavir Nagar, Sumerpur

Consultant

Vipal H Parmar, Consultant histopathologist at neuberg supratech references laboratories, Ahmedabad (NSRL)

Consultant

Bhavana Asit Mehta, Department Histoanatomic Pathology Department, Neuberg Supratech Reference Laboratory, Ahmedabad, Gujarat

Consultant

Shraddha Mehta, Department Of Pathology, Bhagwan Mahavir Hospital, Mahavir Nagar, Sumerpur

Consultant

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Published

2022-03-15

How to Cite

1.
Barolia DK, Singh AP, Bathia HV, Parmar VH, Mehta BA, Mehta S. Rectal atresia with pouch colon without fistula in a female newborn– a rare association: A case report. J Pediatr Adolesc Surg [Internet]. 2022Mar.15 [cited 2022Aug.7];2(1). Available from: http://jpedas.org/ojs/index.php/jpedas/article/view/jpas-102
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